Pathognomonic Oral Profile of Lubinsky-MacGibbon Syndrome for Lowering the Risk of Progressive Renal Failure: Rare Case Report
Author(s): Almoataz Bellah Abdullah Tawfiq Abdel-Bari*, Ahmed Abd El-Latif Mosleh and Khaled Abd El-Hamid Saad
Abstract
Lubinsky-MacGibbon syndrome is an extremely rare condition characterized by defective amelogenesis and bilateral medullary nephrocalcinosis. Because nephrocalcinosis is symptomless even though renal complications may not emerge until late childhood or early adulthood, the pathognomonic orodental findings and panoramic radiographic features present in early childhood play an exclusive role in the early detection of this rare syndrome for better renal prognosis.